Opsoclonus-myoclonus-ataxia Syndrome: A Pediatric Oncology Hospital Experience
نویسندگان
چکیده
Background: Opsoclonus myoclonus ataxia syndrome (OMAS) is a rare, immune-mediated neurological disorder that usually starts in the second year of life. The triad signs composed opsoclonus, and ataxia. In addition, there often irritability sleep disturbance. about 50% children an underlying neuroblastoma.
منابع مشابه
Neuroblastoma and opsoclonus-myoclonus-ataxia syndrome--clinical and pathological characteristics.
INTRODUCTION Opsoclonus-myoclonus-ataxia (OMA) syndrome is the most common paraneoplastic neurological syndrome in childhood. MATERIALS AND METHODS We reviewed the literature and reported on clinical and pathological characteristics of four children with OMA and peripheral neuroblastic tumours. In two of the children the onset of neurological symptoms was connected with a vaccination and in o...
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1 of 1 DESCRIPTION Opsoclonus-Myoclonus syndrome is a rare dyskinesia due to an underlying infectious, metabolic or neoplastic process. 1 It is frequently caused by neuroblastoma in children and breast or lung carcinoma in adults. It is characterised by high amplitude, multidirectional, arrhythmic and conjugate ocular saccadic intrusions without intersaccadic latency causing oscillopsia 2 and i...
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Opsoclonus-myoclonus-ataxia (OMA) syndrome typically presents with chaotic eye movements and myoclonus with some patients exhibiting ataxia and behavioural disturbances. The pathogenesis may be inflammatory with an infectious or paraneoplastic trigger. We present a 13-year-old HIV-infected girl who was initially started on highly active antiretroviral therapy (HAART) in March 2013 with a CD4 co...
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We analyzed the features of opsoclonus syndrome as a manifestation of post viral encephalopathy in 3 patients (one child and 2 adults). This is the first report of opsoclonus-myoclonus syndrome in the Arabian Peninsula. Symptoms appeared a few days after a viral-like illness in all patients. We excluded the possibility of paraneoplastic syndrome as investigations were carried out and follow-up ...
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ژورنال
عنوان ژورنال: Arquivos De Neuro-psiquiatria
سال: 2023
ISSN: ['1678-4227', '0004-282X']
DOI: https://doi.org/10.1055/s-0043-1774451